Creutzfeldt Jakob Disease News and Research

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Creutzfeldt–Jakob disease or CJD (sometimes incorrectly referred to as mad cow disease) is a degenerative neurological disorder (brain disease) that is incurable and invariably fatal. It is the most common among the types of transmissible spongiform encephalopathy found in humans.

Disease associated prion protein oligomers inhibit the 26S proteasome

The rogue prion proteins responsible for diseases like BSE and vCJD can destroy brain cells by blocking the protein recycling process that helps keep cells healthy.

27 Apr 2007

Mad cow disease appears again in Canadian cattle

The Canadian Food Inspection Agency (CFIA) says there has been another case of bovine spongiform encephalopathy (BSE) in Canadian cattle.

12 Feb 2007

Alphanate approved to treat Von Willebrand disease

The U.S. Food and Drug Administration (FDA) has announced the approval of Antihemophilic Factor/von Willebrand Factor Complex (Human), Alphanate.

4 Feb 2007

UK scientists reverse symptoms of mad cow disease

The researchers at University College, London, believe they have found a way to treat the disease in humans as long as it is detected before it has done harm to a large number of brain cells.

1 Feb 2007

Effects of prion disease could be reversed if caught early enough

The researchers said that their findings support developing early treatments that aim to reduce levels of prion protein in the brains of people with prion disease.

31 Jan 2007

Health officials accused over cover up in deaths from vCJD

A cover up on the part of British health authorities meant a man who had been infected with CJD from contaminated blood during a transfusion was not told until he was dying what was really wrong with him.

11 Dec 2006

CJD closes operating theatres in Canada

All surgery at a hospital in Ontario Canada has been halted after it was discovered that a patient undergoing neurosurgery on November 30th may have had the fatal brain-wasting disease Creutzfeldt-Jakob (CJD).

6 Dec 2006

Dr. Google the latest tool to help doctors diagnose unusual cases

In a really interesting study a team of Australian doctors went to the Internet to test the effectiveness and accuracy of the search engine Google when it was presented with a number of symptoms.

13 Nov 2006

British tourist in Hong Kong has mad cow disease

A British tourist in Hong Kong has been struck down with what appears to be mad cow disease.

30 Aug 2006

Factors determining the potential for onward transmission of vCJD via surgical instruments

A study published in the Journal of the Royal Society Interface has been exploring the likelihood that vCJD might be spread via the reuse of surgical instruments, and calls for more data in order to allay fears over the possible transmission of vCJD.

3 Aug 2006

New aspect of prion disease - agent causes heart damage

Until now, prion disease has been thought of as a chronic neurological condition.

9 Jul 2006

New discovery boosts basic understanding of prion infections

Brittleness is often seen as a sign of fragility. But in the case of infectious proteins called prions, brittleness makes for a tougher, more menacing pathogen.

28 Jun 2006

New human genotype may be prone to vCJD

A small study in the British Medical Journal suggests a new human genotype may be prone to variant Creutzfeldt-Jakob disease (vCJD).

6 Jun 2006

vCJD may have infected far more people than previously thought

Scientists at the National CJD Surveillance Unit at the University of Edinburgh say that thousands may be infected with variant Creutzfeldt-Jakob Disease (vCJD) without showing signs or symptoms.

21 May 2006

Transplanted human tissue linked to seven cases of Creutzfeldt-Jakob disease in the UK

Seven cases of Creutzfeldt-Jakob disease (CJD) associated with transplanted human tissue have occurred in the UK over a period of 33 years, reveals a study published ahead of print in the Journal of Neurology Neurosurgery and Psychiatry.

25 Apr 2006

Increase in variant Creutzfeldt Jakob Disease predicted

According to the latest research far more people may be at risk of contracting variant Creutzfeldt Jakob Disease (vCJD) than previously thought.

28 Mar 2006

Third U.S. case of mad cow disease

According to the U.S. Department of Agriculture routine tests have revealed a third U.S. case of mad cow disease.

13 Mar 2006

Research suggests that a common mechanism may underlie a variety of protein folding diseases

Misfolded and damaged proteins are common to all human neurodegenerative diseases. Clumps of these aggregated proteins destroy neurons within the brain and cause disease.

16 Feb 2006

Emerging infectious agents pose new risks for people with bleeding disorders

An international team of scientists, including a hematologist from Thomas Jefferson University in Philadelphia, has concluded that people with bleeding disorders such as hemophilia remain at risk from emerging infectious agents in plasma and blood transfusions. For this reason, recombinant therapies, that is, those produced in the laboratory, must always be an option

16 Feb 2006

Deer a possible source of "mad cow like" disease

A University of Kentucky researcher has warned that eating deer could put people at risk of a disease similar to bovine spongiform encephalopathy (BSE) commonly known as mad cow disease.

30 Jan 2006